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Volume 4 Supplement 1

Unmet needs in Pulmonary Hypertension associated with Adult Congenital Heart Disease (ACHD-PH)

Research

Publication of this supplement is sponsored by Actelion Pharmaceuticals UK Ltd, who had no influence on manuscript writing. Medical writing support for manuscripts was provided by nspm ltd, Meggen, Switzerland and was also funded by Actelion Pharmaceuticals UK Ltd. The articles have undergone the journal's standard peer review process. RT (Supplement Editor) has received unrestricted educational, travel and research grants from Actelion. RT declares similar grants from Pfizer, GSK and Bayer. JO (Supplement Editor) declares no competing interests.

Edited by Robert Tulloh and James Oliver

  1. Pulmonary hypertension is not uncommon in adult patients with congenital heart disease and can significantly affect their exercise capacity, quality of life and prognosis. Timely identification and management ...

    Authors: Heba Nashat, Carla Favoccia, Andrew Constantine and Konstantinos Dimopoulos
    Citation: Journal of Congenital Cardiology 2020 4(Suppl 1):22
  2. Pulmonary hypertension (PH) is commonly seen in adults who have congenital heart disease (CHD). Therapy is available for pulmonary arterial hypertension (PAH) and has greatly benefitted many patients with PAH ...

    Authors: Nathalie Liew, Zoya Rashid and Robert Tulloh
    Citation: Journal of Congenital Cardiology 2020 4(Suppl 1):21
  3. A structured transition provides a framework of care that bridges the gap between paediatric and adult medicine. It is essential for achieving continuity of care and providing support and education around the ...

    Authors: Andrew Constantine, Robert M. R. Tulloh, Rebecca Turquet, Konstantinos Dimopoulos and Shahin Moledina
    Citation: Journal of Congenital Cardiology 2020 4(Suppl 1):9
  4. This is a case report of a patient diagnosed with Eisenmenger syndrome in adult life.

    Authors: Heba Nashat, Andrew Constantine and Konstantinos Dimopoulos
    Citation: Journal of Congenital Cardiology 2020 4(Suppl 1):14
  5. Eisenmenger syndrome is a multisystem disorder, characterised by a significant cardiac defect, severe pulmonary hypertension and long-standing cyanosis. Despite the availability of pulmonary hypertension thera...

    Authors: Rosaria Barracano, Heba Nashat, Andrew Constantine and Konstantinos Dimopoulos
    Citation: Journal of Congenital Cardiology 2020 4(Suppl 1):13
  6. An increasing number of patients with previously repaired congenital heart disease (CHD) present with pulmonary arterial hypertension (PAH). This can occur immediately after repair (residual PAH) or years later.

    Authors: Margarita Brida, Carla Favoccia, Andrew Constantine and Konstantinos Dimopoulos
    Citation: Journal of Congenital Cardiology 2020 4(Suppl 1):12
  7. Although there are some data on how to manage and treat patients with Eisenmenger syndrome due to simple cardiac defects, little evidence exists to guide best management of pulmonary vascular disease in cases ...

    Authors: Zoya Rashid and Robert Tulloh
    Citation: Journal of Congenital Cardiology 2020 4(Suppl 1):18
  8. The Fontan circulation is a palliative procedure for patients born with a single ventricle physiology. The Fontan circulation is associated with significant late morbidity commonly including atrial arrhythmias.

    Authors: Paul Clift
    Citation: Journal of Congenital Cardiology 2020 4(Suppl 1):23
  9. Current guidelines for the peri-operative assessment and management are not sufficient to allow effective risk assessment and management of the patient with pulmonary arterial hypertension associated with cong...

    Authors: Andrew Constantine and Paul Clift
    Citation: Journal of Congenital Cardiology 2020 4(Suppl 1):15
  10. Management of patients with pulmonary arterial hypertension associated with congenital heart disease and trisomy 21 is complex due to uncertainty over the best first-line agent to use for treatment, and the ou...

    Authors: Zoya Rashid and Robert Tulloh
    Citation: Journal of Congenital Cardiology 2020 4(Suppl 1):19