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Table 2 Critical care strategies for treatment of PH [33]

From: Down syndrome and congenital heart disease: perioperative planning and management

Encourage

Avoid

1. Anatomic investigation

1. Residual anatomic disease

2. Right to left atrial pop off

2. Intact atrial septum

3. Sedation/analgesia

3. Agitation/pain

4. Moderate hyperventilation

4. Respiratory acidosis

5. Moderate alkalosis

5. Metabolic acidosis

6. Adequate inspired oxygen

6. Alveolar hypoxia

7. Normal lung volumes

7. Atelectasis or overdistension

8. Optimal hematocrit

8. Excessive hematocrit

9. Inotropic support

9. Low output and coronary perfusion

10. Pulmonary vasodilators

10. Pulmonary vasoconstrictors